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Table 3 Clinical characteristics of 16 patients with RAA

From: Long-term follow-up of retinal amyloid angiopathy in a large Chinese family with hereditary amyloid transthyretin

Patient

Gender

Laterality

Age at VO (years)

Age at PPV (years)

BCVA before surgery

BCVA after surgery

BCVA at final visit

Complications associated with RAA

Duration of hATTR (years)

Staging of RAA at final visit

IV:2

F

R

46

56

CF/40 cm

20/50

HM/40 cm

Choroidal hemorrhage

12

Clinical stage

L

55

58

CF/40 cm

20/50

20/100

N

12

Progressive stage

IV:4

F

R

52

55

CF/40 cm

20/50

20/50

N

5

Early stage

L

52

55

CF/40 cm

20/50

20/50

N

5

Early stage

IV:8

F

R

62

64

20/50

20/50

20/40

N

5

Early stage

L

59

62

LP

20/50

20/50

N

5

Early stage

IV:9

M

R

46

48

CF/40 cm

20/20

HM

Neovascular glaucoma

15

Clinical stage

L

46

48

CF/40 cm

20/25

LP

Neovascular glaucoma

15

Clinical stage

IV:11

M

R

40

43

20/250

20/50

LP

Retinal detachment

13

Clinical stage

L

37

40

CF/40 cm

20/100

HM/40 cm

Neovascular glaucoma

13

Clinical stage

IV:16

F

R

54

56

20/50

20/32

20/32

N

2

Early stage

L

54

56

20/50

20/32

20/32

N

2

Early stage

IV:19

M

R

41

43

CF/40 cm

20/40

20/100

Neovascular glaucoma

12

Clinical stage

L

38

40

HM/40 cm

20/40

CF/40 cm

Neovascular glaucoma

12

Clinical stage

IV:22

M

R

52

54

CF/40 cm

20/40

20/50

Neovascular glaucoma

13

Clinical stage

L

52

54

CF/40 cm

20/50

20/80

Neovascular glaucoma

13

Clinical stage

IV:40

M

R

61

63

CF/40 cm

20/32

20/32

N

4

Early stage

L

63

65

20/400

20/32

20/32

N

4

Early stage

IV:45

F

R

41

44

CF/40 cm

20/50

20/70

Neovascular glaucoma

10

Clinical stage

L

42

51

CF/40 cm

20/100

20/100

N

10

Progressive stage

V:3

M

R

42

NA

CF/40 cm

NA

CF

N

3

Early stage

L

42

45

HM/40 cm

20/40

20/32

N

3

Early stage

V:6

F

R

40

55

HM/40 cm

20/200

NLP

Retinal detachment

18

Clinical stage

L

40

55

HM/40 cm

20/200

20/200

N

18

Progressive stage

V:23

M

R

57

58

20/100

20/20

20/20

N

4

Early stage

L

54

56

20/32

20/32

20/32

N

4

Early stage

V:58

M

R

41

44

CF/40 cm

20/50

20/25

Neovascular glaucoma

11

Clinical stage

L

43

46

CF/40 cm

20/40

20/100

Neovascular glaucoma

11

Clinical stage

V:60

M

R

52

55

20/63

20/50

20/50

N

8

Progressive stage

L

58

60

20/100

20/32

20/32

N

8

Progressive stage

V:65

F

R

39

42

CF/40 cm

20/40

20/40

N

10

Progressive stage

L

39

42

CF/40 cm

20/25

20/32

N

10

Progressive stage

  1. R: right; L: left; M: male; F: female. N: no complications associated with RAA were diagnosed; NA: not applicable