Patient | Gender | Laterality | Age at VO (years) | Age at PPV (years) | BCVA before surgery | BCVA after surgery | BCVA at final visit | Complications associated with RAA | Duration of hATTR (years) | Staging of RAA at final visit |
---|---|---|---|---|---|---|---|---|---|---|
IV:2 | F | R | 46 | 56 | CF/40 cm | 20/50 | HM/40 cm | Choroidal hemorrhage | 12 | Clinical stage |
L | 55 | 58 | CF/40 cm | 20/50 | 20/100 | N | 12 | Progressive stage | ||
IV:4 | F | R | 52 | 55 | CF/40 cm | 20/50 | 20/50 | N | 5 | Early stage |
L | 52 | 55 | CF/40 cm | 20/50 | 20/50 | N | 5 | Early stage | ||
IV:8 | F | R | 62 | 64 | 20/50 | 20/50 | 20/40 | N | 5 | Early stage |
L | 59 | 62 | LP | 20/50 | 20/50 | N | 5 | Early stage | ||
IV:9 | M | R | 46 | 48 | CF/40 cm | 20/20 | HM | Neovascular glaucoma | 15 | Clinical stage |
L | 46 | 48 | CF/40 cm | 20/25 | LP | Neovascular glaucoma | 15 | Clinical stage | ||
IV:11 | M | R | 40 | 43 | 20/250 | 20/50 | LP | Retinal detachment | 13 | Clinical stage |
L | 37 | 40 | CF/40 cm | 20/100 | HM/40 cm | Neovascular glaucoma | 13 | Clinical stage | ||
IV:16 | F | R | 54 | 56 | 20/50 | 20/32 | 20/32 | N | 2 | Early stage |
L | 54 | 56 | 20/50 | 20/32 | 20/32 | N | 2 | Early stage | ||
IV:19 | M | R | 41 | 43 | CF/40 cm | 20/40 | 20/100 | Neovascular glaucoma | 12 | Clinical stage |
L | 38 | 40 | HM/40 cm | 20/40 | CF/40 cm | Neovascular glaucoma | 12 | Clinical stage | ||
IV:22 | M | R | 52 | 54 | CF/40 cm | 20/40 | 20/50 | Neovascular glaucoma | 13 | Clinical stage |
L | 52 | 54 | CF/40 cm | 20/50 | 20/80 | Neovascular glaucoma | 13 | Clinical stage | ||
IV:40 | M | R | 61 | 63 | CF/40 cm | 20/32 | 20/32 | N | 4 | Early stage |
L | 63 | 65 | 20/400 | 20/32 | 20/32 | N | 4 | Early stage | ||
IV:45 | F | R | 41 | 44 | CF/40 cm | 20/50 | 20/70 | Neovascular glaucoma | 10 | Clinical stage |
L | 42 | 51 | CF/40 cm | 20/100 | 20/100 | N | 10 | Progressive stage | ||
V:3 | M | R | 42 | NA | CF/40 cm | NA | CF | N | 3 | Early stage |
L | 42 | 45 | HM/40 cm | 20/40 | 20/32 | N | 3 | Early stage | ||
V:6 | F | R | 40 | 55 | HM/40 cm | 20/200 | NLP | Retinal detachment | 18 | Clinical stage |
L | 40 | 55 | HM/40 cm | 20/200 | 20/200 | N | 18 | Progressive stage | ||
V:23 | M | R | 57 | 58 | 20/100 | 20/20 | 20/20 | N | 4 | Early stage |
L | 54 | 56 | 20/32 | 20/32 | 20/32 | N | 4 | Early stage | ||
V:58 | M | R | 41 | 44 | CF/40 cm | 20/50 | 20/25 | Neovascular glaucoma | 11 | Clinical stage |
L | 43 | 46 | CF/40 cm | 20/40 | 20/100 | Neovascular glaucoma | 11 | Clinical stage | ||
V:60 | M | R | 52 | 55 | 20/63 | 20/50 | 20/50 | N | 8 | Progressive stage |
L | 58 | 60 | 20/100 | 20/32 | 20/32 | N | 8 | Progressive stage | ||
V:65 | F | R | 39 | 42 | CF/40 cm | 20/40 | 20/40 | N | 10 | Progressive stage |
L | 39 | 42 | CF/40 cm | 20/25 | 20/32 | N | 10 | Progressive stage |